A Case of idiopathic portal hypertension complicating chronic non-suppurative destructive cholangitis and systemic sclerosis.

Idiopathic portal hypertension complicating systemic sclerosis: a case report

BACKGROUND Patients with systemic sclerosis may develop mild abnormalities of liver function tests. More serious hepatic involvement has been well documented but is rare. Idiopathic portal hypertension had been reported only in a few female patients with systemic sclerosis. CASE PRESENTATION An 82-year-old man with known systemic sclerosis presented with melaena. Urgent gastroscopy revealed o...

Idiopathic portal hypertension complicating systemic sclerosis: Case report

Idiopathic non-cirrhotic portal hypertension

Idiopathic non-cirrhotic portal hypertension Sith Siramolpiwat1,2, Susana Seijo3* 1Chulabhorn International College of Medicine, Thammasat University, Pathumthani, 12120, Thailand 2Division of Gastroenterology, Department of Internal Medicine, Faculty of Medicine, Thammasat University, Pathumthani, 12120, Thailand 3CTO, Department of Medicine, Icahn School of Medicine at Mount Sinai, New York, ...

Idiopathic non-cirrhotic portal hypertension: a review

Idiopathic non-cirrhotic portal hypertension (INCPH) is a rare disease characterized of intrahepatic portal hypertension in the absence of cirrhosis or other causes of liver disease and splanchnic venous thrombosis. The etiology of INCPH can be classified in five categories: 1) immunological disorders (i.e. association with common variable immunodeficiency syndrome, connective tissue diseases, ...

Presentation of Idiopathic Portal Hypertension in a Patient with Limited Systemic Sclerosis

......................................... Received: 06-12-13 Accepted: 21-07-14 Abstract Systemic sclerosis is a multisystem rheumatic autoimmune disorder characterized by fibrosis of the skin and many other organs. The gastrointestinal tract is the second cause of systemic compromise of this disease, but idiopathic portal hypertension is an extremely rare condition in these patients. We descri...